Angioedema hereditário com deficiência de inibidor de C1 esterase e parada cardiorrespiratória: relato de caso

Abstract

Objective: report the clinical picture of a patient with a previous diagnosis of hereditary angioedema with C1 esterase inhibitor deficiency, associated with cardiorespiratory arrest in an emergency department. Case report: female patient, 23 years old, with previous diagnosis of hereditary angioedema with deficiency of C1 esterase inhibitor, complained of edema on the face and lips, for three days, evolving with sudden worsening and cardiorespiratory arrest. Conclusion: in hereditary angioedema, there may be a sudden, unfavorable worsening, even with cardiorespiratory arrest, which implies early recognition of its potential severity. Clinical improvement could be observed after the use of fresh frozen plasma, performed in an intensive support location.